A three year old girl with a left renal teratoid Wilms tumor is reported.
The tumor was located both inside and outside the kidney parenchyme, to form a well
encapsulated mass containing two lobulated solid and cystic masses. The tumor consists
predominantly of otherwise typical Wilms tumor irregularly mixed with teratoid tissue
elements such as intestinal tract, mucous glands with argentaffin cells, goblet cells and
transitional epithelium. These heterologous elements were regarded as diverse epithelial
differentiation of totipotent cells in certain nephrogenetic period, and this tumor was
considered to be hest called "teratoid Wilms tumor".
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